文献简介

出版社:Dermatology Online Journal, 18(8)

作  者:Ryokichi Irisawa MD, Masashi Yamazaki MD PhD, Toshiyuki Yamamoto MD PhD

编  号:

关键字:porokeratosis plantaris palmaris et disseminata

年  份:2012   点击量:1062

文献摘要 全文翻译

Abstract
Porokeratosis plantaris palmaris et disseminata (PPPD) is a quite rare variant of porokeratosis. We report a 56-year-old male patient. He first noted brownish, asymptomatic, annular macules scattered on the trunk and extremities at about age 31 and these skin lesions, continued to increase in number. Ten years prior to presentation, similar lesions appeared on the palms. About one to two years ago, the patient noted painful wart-like, keratotic punctuate papules 2-3 mm in diameter on the soles, which disturbed walking. Histological examination showed the characteristic feature of the cornoid lamella. The family tree of this patient showed an autosomal dominant mode of transmission. We review sixteen typical cases of PPPD previously reported in the English literature.
摘要
合并播散性掌跖汗孔角化症(PPPD)是汗孔角化症中极其罕见的一种临床类型。本文报道了一例56岁的男性患者病例。其躯干、四肢无症状、褐色环状斑疹25年余,且皮损数目逐年渐增。近10年掌部出现类似皮疹。约一两年前,其跖部出现直径为2-3mm的疼痛性疣样的角化性点状丘疹,影响行走。组织学检查显示角样板结构特征。该患者家谱显示常染色体显性遗传模式。本文回顾了16例英文文献中报道的PPPD的典型病例。