文献资料 > 淀粉样变病
KTP Laser in Laryngeal Amyloidosis: Five Cases with Review of Literature2014.12.30
在喉淀粉样变病的KTP激光:5例病例与文献综述
为了研究临床表现和综述喉淀粉样变病的治疗方法。为了研究KTP532激光对切除喉淀粉样变病的疗效。2001年1月到2010年2月之间,研究在一个三级保健医院中我们所在的部门进行。我们报道了患有声音嘶哑和局部喉病变的5名患者。在3名患者中,活检证实显微内窥镜下通过KTP532激...
Update on treatment of light chain amyloidosis2014.12.30
Light chain amyloidosis is the most common type of amyloidosis as a consequence of protein misfolding of aggregates composed of amyloid fibrils. The clinical features are dependent on the organs involved, typically cardiac, renal, hepatic, peripheral...
Secondary intestinal amyloidosis presenting intractable hematochezia: a case report and literature review2014.12.30
Abstract: Amyloidosis is characterized by an extracellular deposition of insoluble fibrils. Amyloid deposition caused various clinical symptoms associated with affected organs. Secondary amyloidosis without renal involvement and chronic inflammatory ...
Primary Localized Amyloidosis of Urinary Bladder: A Case Report and Review of Literature2014.12.30
Amyloidosis is a disorder of protein metabolism characterized by extracellular deposition of abnormal protein fibrils. It may either be localized to any organ or systematically distributed throughout the body. The biochemical nature of proteins varie...
Primary Amyloidosis of the Breast Presenting as a Solitary Nodule: Case Report and Review of the Literature2014.12.30
Background: Amyloidosis of the breast is an unusual diagnosis.Overall, only 2 major case series have been published in the literature sincethe time amyloidosis was first reported in 1973, highlighting the rare natureof this disease. Clinically, the p...
Novel Drugs Targeting Transthyretin Amyloidosis2014.12.30
针对转甲状腺素蛋白淀粉样变性的新型药物
转甲状腺素蛋白淀粉样变病(ATTR)要么是与转甲状腺素蛋白基因的突变有关的导致神经病和/或心肌病的一种遗传性疾病,要么是导致限制性心肌病的一种老年人后天性疾病。这种疾病的患病率比以前认为的高,并且医生之间对它的关注可能会增加,尤其是心脏科医生。直到最近还没...
Targeted Treatment for Amyloidosis2014.12.30
Amyloid is a pathological extracellulardeposit with a fibrillar ultrastructure (reviewed in ). In addition to theamyloid fibrils that constitute the bulk of the deposits, abundant glycosaminoglycansand proteoglycans are always present, as is the non-...
Successful treatment of lichen amyloidosis using a CO2 surgical laser2014.12.30
ABSTRACT: Lichenamyloidosis (LA) is a type of primary localized cutaneous amyloidosischaracterized by multiple pruritic discrete hyperkeratotic papules with amyloiddeposition in the papillary dermis. Two patients with LA had been treated withtopical ...
Prognostic stratification andtreatmentofcardiaclight chain amyloidosis:Anarrowpathinthejungle2014.12.30
Amyloid lightchain(AL)amyloidosisisthemost common formofsystemicamyloidosis,withanincidence of approximately3,000newcasesperyearintheUnited States and5,000intheEuropeanUnion. It issustainedby an indolentcloneofdyscrasicplasmacellsthatsynthesizes an e...
Diagnostic Approach to Cardiac Amyloidosis2014.12.30
Amyloidosisis a relatively rare disease that may be underdiagnosed and could affect theentire human body. Many organs may be affected, which could increase themorbidity and mortality. Cardiac involvement is the leading cause of poorprognosis. Patient...
An evaluation of Congo red fluorescence for the diagnosis of amyloidosis2014.12.30
刚果红荧光实验对淀粉样变病的诊断的评价
在偏振光下刚果红染色苹果绿双折射是用于检测淀粉样蛋白的最常用的方法;然而,它有局限性。本研究的目的是评估是否通过荧光显微镜(FM)的刚果红染色的检查能够显著提高诊断率。刚果红染色的组织切片通过有无偏光镜的光学显微镜(LM)与德州仪器红色滤光片的荧光显微镜...
Plerixafor and G-CSF for autologous stem cell mobilization in AL amyloidosis2014.12.30
Risk-adapted melphalan and SCT (RA-SCT) isconsidered a standard therapy for selected patients with systemic ALamyloidosis (AL), with median OS exceeding 10 years when used as initial therapy.1With this approach, peri-transplant mortality has been red...
Osteopontin: a novel predictor of survival in patients with systemic light-chain amyloidosis2014.12.29
Background: Troponin-T (cTnT) and NT-proBNP provide prognostic information inlight-chain amyloidosis (AL). Thus, these biomarkers are widely used inclinical routine for risk stratification. Recently, plasma level of osteopontin(OPN), a secreted phosp...
Interleukin-1 signaling pathway as a therapeutic target in transthyretin amyloidosis2014.12.29
Introduction: Inflammation is a keypathological hallmark of several neurodegenerative disorders includingAlzheimer’s disease, Parkinson’s disease and familial amyloidoticpolyneuropathy (FAP). Among all inflammatory cytokines associated with FAP,IL-...
Cardiac magnetic resonance evaluation of left ventricular remodelling distribution in cardiac amyloidosis2014.12.29
Background Cardiac amyloidosis(CA) is associated with typical morphological features on echocardiography, includingconcentric LV hypertrophy (LVH). Cardiac magnetic resonance (CMR) canaccurately depict anatomy in different cardiomyopathies. Our aim w...
共有20条记录  当前第1页  首页 上一页 下一页 尾页